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Nephrol Dial Transplant (1999) 14: 2775-2776
© 1999 European Renal Association-European Dialysis and Transplant Association

Letters

Unilateral form of polycystic kidney disease

Bernard Branger

Nephrology Department, University Hospital, 5 rue Hoche, Nîmes cedex 4, France

Sir,

We report the case of an unusual form of adult polycystic renal disease (APKD) observed in Mr M.V., a 72-year-old outpatient.

Fifteen years previously, the finding of arterial hypertension lead to a renal echography showing a grossly enlarged left kidney with multiple and diffuse cysts. A repeat echography in July 1998 confirmed the finding: the left kidney measured 20x12 cm. The cysts were distributed homogeneously throughout the cortical and the medullary regions. These cysts were spheric and unilocular, and ranged from 1 mm to 5 cm. In contrast, the right kidney was normal sized (12x6 cm) with five isolated cysts (three in the medulla, two in the cortex, their size ranged from 1 to 3 cm). The echography of the liver was normal. An intravenous pyelography confirmed the echographic features with a normal pyelogram of the right kidney.

The father of this patient died from `uraemia' in 1968, when he was 69 years old. The patient is his only child and has a single son.

The clinical examination showed a Caucasian male patient of 75.6 kg weight and 163.5 cm height. Arterial pressure was 140/90 mmHg. Clinical examination was normal with the exception of an enlarged prostatic gland.

Serum creatinine was 105.3 µmol/l, urea 6.85 mmol/l, the ionogram was normal as was the blood cell count. Proteinuria or haematuria were not detected.

This clinical observation raises the question of the existence of `adult unilateral' PKD or a new type of cystic kidney disease. DNA analysis was not possible in our institution but DNA samples are kept in the deep freezer.

Notes

Editor's note

The case is reminiscent of the report of Hwang et al. (Nephrol Dial Transplant 1999; 14: 1999–2003)

References

  1. Tisher CC, Brenner BM. Renal Pathology (2nd edn) J. B. Lippincott Company, Philadelphia 1994

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